A rare case of Creutzfeldt-Jakob disease
Dr. Saumya is reporting a rare case of Creutzfeldt-Jakob disease. Share your views on the case & learn new things Follow us for more such updates!
A VERY RARE CASE OF Creutzfeldt-Jakob DISEASE IS VERY WELL HANDLED BY @Dr. Saumya Mittal WITH ELABORATIVE PRESENTATION ABOUT INTRODUCTION, CASE PROFILE & HISTORY, EXAMINATION FINDINGS, INVESTIGATIONS, DIFFERENTIAL DIAGNOSIS, MANAGEMENT & KEY LEARNINGS. THANKS FOR SHARING.
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Eating beef and beef products contaminated with the infectious agent of bovine spongiform encephalopathy (BSE) is the main cause of VCJD where as Classical CJD has no such connection . The incidence is 1 to 2 per million a rare disease . 1. The CJD has a very long history causing diffuse cortical neuronal atrophy manifesting as dementia . Here the history is just 3 months only. 2 .The family history is negative here . Affected parents have 50%chance of transmission of CJD . So it should be non genetic non varient type of CJD. 3. Diffuse atrophy of brain is common but here there is a band of cortical atrophy in MRIThe 4 .short history is suggestive of a Vasular dementia., than chronic CjD . 5. What is the clinching diagnostic feature to call it CJD , in this case presented , Sir ?
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Very informative and knowledge boosting educational presentation on Creutzfeldt -Jakob disease. Causes, symptoms, Case Profile & History, Vitals, Neurologic Examinations, Investigations, Differential Diagnosis and Managements are very informative. Thanks Dr Saumya H Mittal Sir sharing very informative and useful presentation with us.
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Dr Saumya H.Mittal - Consulting neurologist have presented a rare case of Creutzfeldt - Jakob disease- a progressive & fatal disease with no treatment. But at least we think of how we can prevent transmission How can people avoid spreading the disease. To reduce the already very low risk of CJD transmission from one person to another, people should never donate blood, tissues, or organs if they have suspected or confirmed CJD, or if they are at increased risk because of a family history of the disease, a dura mater graft, or other factor. Normal sterilization procedures such as cooking, washing, and boiling do not destroy prions. Although there is no evidence that caregivers, healthcare workers, and those who prepare bodies for funerals and cremation have increased risk of prion diseases when compared to general population, they should take the following precautions when they are working with a person with CJD: Cover cuts and abrasions with waterproof dressings. Wear surgical gloves when handling the person’s tissues and fluids or dressing any wounds. Avoid cutting or sticking themselves with instruments contaminated by the person’s blood or other tissues. Use disposable bedclothes and other cloth for contact with the person.If disposable materials are not available, regular cloth should be soaked in undiluted chlorine bleach for an hour or more, and then washed in a normal fashion after each use. Use face protection if there is a risk of splashing contaminated material such as blood or cerebrospinal fluid. Soak instruments that have come in contact with the person in undiluted chlorine bleach for an hour or more, then use an autoclave (pressure cooker) to sterilize them in distilled water for at least one hour . Congratulations- Sir for enlightening us Thanks
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